Annotation Detail

Information
Associated Genes
MEFV
Associated Variants
MEFV p.Glu148Val (p.E148V) ( ENST00000536379.5, ENST00000219596.6, ENST00000339854.8, ENST00000541159.5 )
MEFV p.Glu148Val (p.E148V) ( ENST00000219596.6, ENST00000339854.8, ENST00000536379.5, ENST00000541159.5 )
Associated Disease
Acute febrile neutrophilic dermatosis
Source Database
ClinVar
Description
NM_000243.3(MEFV):c.443A>T (p.Glu148Val) AND Acute febrile neutrophilic dermatosis
ClinVar Allele ID
17593
ClinVar RefSeq Alternation Syntax
NM_000243.3:c.443A>T
ClinVar RefSeq Alternation Syntax
NM_001198536.2:c.277+1686A>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2023-02-08
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003125826
ClinVar Disease
Acute febrile neutrophilic dermatosis
Observed Origin Sample
germline
Drugs