Annotation Detail

Information
Associated Genes
NR5A1
Associated Variants
NR5A1 p.Pro129Leu (p.P129L) ( ENST00000373588.9, ENST00000620110.4 )
NR5A1 p.Pro129Leu (p.P129L) ( ENST00000373588.9, ENST00000620110.4 )
Associated Disease
Oligosynaptic infertility 46,XY disorder of sex development
Source Database
ClinVar
Description
NM_004959.5(NR5A1):c.386C>T (p.Pro129Leu) AND multiple conditions
ClinVar Allele ID
38458
ClinVar RefSeq Alternation Syntax
NM_004959.5:c.386C>T
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2023-12-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003105833
ClinVar Disease
46,XY disorder of sex development
ClinVar Disease
Oligosynaptic infertility
Observed Origin Sample
germline
Drugs