Annotation Detail

Information
Associated Genes
DICER1
Associated Variants
DICER1 p.Ser911Thr (p.S911T) ( ENST00000696736.1, ENST00000529720.2, ENST00000527414.5, ENST00000343455.8, ENST00000674628.2, ENST00000393063.6, ENST00000541352.5, ENST00000532939.3, ENST00000526495.6, ENST00000696737.1, ENST00000531162.7 )
DICER1 p.Ser911Thr (p.S911T) ( ENST00000343455.8, ENST00000393063.6, ENST00000526495.6, ENST00000527414.5, ENST00000529720.2, ENST00000531162.7, ENST00000532939.3, ENST00000541352.5, ENST00000674628.2, ENST00000696736.1, ENST00000696737.1 )
Associated Disease
DICER1-related tumor predisposition
Source Database
ClinVar
Description
NM_177438.3(DICER1):c.2732G>C (p.Ser911Thr) AND DICER1-related tumor predisposition
ClinVar Allele ID
2187153
ClinVar RefSeq Alternation Syntax
NM_001395680.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395682.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395693.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395683.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395690.1:c.2327G>C
ClinVar RefSeq Alternation Syntax
NR_172720.1:n.3077G>C
ClinVar RefSeq Alternation Syntax
NR_172716.1:n.3077G>C
ClinVar RefSeq Alternation Syntax
NM_001291628.2:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395681.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395692.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395679.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_030621.4:c.2732G>C
ClinVar RefSeq Alternation Syntax
NR_172719.1:n.3077G>C
ClinVar RefSeq Alternation Syntax
NR_172715.1:n.3150G>C
ClinVar RefSeq Alternation Syntax
NM_177438.3:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395686.1:c.2450G>C
ClinVar RefSeq Alternation Syntax
NR_172717.1:n.3244G>C
ClinVar RefSeq Alternation Syntax
NR_172718.1:n.3244G>C
ClinVar RefSeq Alternation Syntax
NM_001395678.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395689.1:c.2327G>C
ClinVar RefSeq Alternation Syntax
NM_001271282.3:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395677.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395688.1:c.2327G>C
ClinVar RefSeq Alternation Syntax
NM_001395687.1:c.2327G>C
ClinVar RefSeq Alternation Syntax
NM_001395684.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001195573.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395691.1:c.2165G>C
ClinVar RefSeq Alternation Syntax
NM_001395694.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395695.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395685.1:c.2732G>C
ClinVar RefSeq Alternation Syntax
NM_001395697.1:c.1049G>C
ClinVar RefSeq Alternation Syntax
NM_001395696.1:c.2327G>C
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2022-05-05
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV003044942
ClinVar Disease
DICER1-related tumor predisposition
Observed Origin Sample
germline
Drugs