Annotation Detail

Information
Associated Genes
KDM6A
Associated Variants
KDM6A p.Arg571Ter (p.R571*) ( ENST00000543216.6, ENST00000377967.9, ENST00000382899.9, ENST00000536777.6, ENST00000611820.5, ENST00000674586.1, ENST00000674867.1, ENST00000683021.1 )
KDM6A p.Arg571Ter (p.R571*) ( ENST00000377967.9, ENST00000382899.9, ENST00000536777.6, ENST00000543216.6, ENST00000611820.5, ENST00000674586.1, ENST00000674867.1, ENST00000683021.1 )
Associated Disease
Inborn genetic diseases
Source Database
ClinVar
Description
NM_001291415.2(KDM6A):c.1711C>T (p.Arg571Ter) AND Inborn genetic diseases
ClinVar Allele ID
48506
ClinVar RefSeq Alternation Syntax
NM_001291421.2:c.667C>T
ClinVar RefSeq Alternation Syntax
NM_001291416.2:c.1576C>T
ClinVar RefSeq Alternation Syntax
NM_001291417.2:c.1420C>T
ClinVar RefSeq Alternation Syntax
NM_001291415.2:c.1711C>T
ClinVar RefSeq Alternation Syntax
NR_111960.2:n.1838C>T
ClinVar RefSeq Alternation Syntax
NM_001291418.2:c.1318C>T
ClinVar RefSeq Alternation Syntax
NM_021140.4:c.1555C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-09-07
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002513317
ClinVar Disease
Inborn genetic diseases
Observed Origin Sample
germline
Drugs