Annotation Detail

Information
Associated Genes
ABCA4
Associated Variants
ABCA4 c.5714+5G>A ( ENST00000370225.4 )
ABCA4 c.5714+5G>A ( ENST00000370225.4 )
Associated Disease
age related macular degeneration 2 Severe early-childhood-onset retinal dystrophy cone-rod dystrophy 3 retinitis pigmentosa 19
Source Database
ClinVar
Description
NM_000350.3(ABCA4):c.5714+5G>A AND multiple conditions
ClinVar Allele ID
105292
ClinVar RefSeq Alternation Syntax
NM_000350.3:c.5714+5G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-01-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002498458
ClinVar Disease
Age related macular degeneration 2
ClinVar Disease
Severe early-childhood-onset retinal dystrophy
ClinVar Disease
Cone-rod dystrophy 3
ClinVar Disease
Retinitis pigmentosa 19
Observed Origin Sample
unknown
Drugs