Annotation Detail

Information
Associated Genes
TTR
Associated Variants
TTR p.Ala117Ser (p.A117S) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
TTR p.Ala117Ser (p.A117S) ( ENST00000237014.8, ENST00000610404.5, ENST00000649620.1 )
Associated Disease
carpal tunnel syndrome 1 Familial amyloid neuropathy Hyperthyroxinemia, dystransthyretinemic
Source Database
ClinVar
Description
NM_000371.4(TTR):c.349G>T (p.Ala117Ser) AND multiple conditions
ClinVar Allele ID
28507
ClinVar RefSeq Alternation Syntax
NM_000371.4:c.349G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-05-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002496359
ClinVar Disease
Hyperthyroxinemia, dystransthyretinemic
ClinVar Disease
Familial amyloid neuropathy
ClinVar Disease
Carpal tunnel syndrome 1
Observed Origin Sample
unknown
Drugs