Annotation Detail

Information
Associated Genes
CFB C2
Associated Variants
ENSG00000244255 c.1571-126T>A, CFB p.Leu9His (p.L9H) ( ENST00000425368.7, ENST00000483004.2, ENST00000698628.1 )
ENSG00000244255 c.1571-126T>A, CFB p.Leu9His (p.L9H) ( ENST00000425368.7, ENST00000483004.2, ENST00000698628.1 )
Associated Disease
Atypical hemolytic-uremic syndrome with B factor anomaly Complement factor b deficiency age related macular degeneration 14
Source Database
ClinVar
Description
NM_001710.6(CFB):c.26T>A (p.Leu9His) AND multiple conditions
ClinVar Allele ID
31116
ClinVar RefSeq Alternation Syntax
NM_001710.6:c.26T>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2022-04-25
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002490378
ClinVar Disease
Age related macular degeneration 14
ClinVar Disease
Complement factor b deficiency
ClinVar Disease
Atypical hemolytic-uremic syndrome with B factor anomaly
Observed Origin Sample
unknown
Drugs