Annotation Detail

Information
Associated Genes
PKD1
Associated Variants
PKD1 p.Cys508Arg (p.C508R) ( ENST00000423118.5, ENST00000262304.9 )
PKD1 p.Cys508Arg (p.C508R) ( ENST00000262304.9, ENST00000423118.5 )
Associated Disease
Polycystic kidney disease, adult type
Source Database
ClinVar
Description
NM_001009944.3(PKD1):c.1522T>C (p.Cys508Arg) AND Polycystic kidney disease, adult type
ClinVar Allele ID
793626
ClinVar RefSeq Alternation Syntax
NM_001009944.3:c.1522T>C
ClinVar RefSeq Alternation Syntax
NM_000296.4:c.1522T>C
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-10-11
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002489472
ClinVar Disease
Polycystic kidney disease, adult type
Observed Origin Sample
unknown
Drugs