Annotation Detail

Information
Associated Genes
XRCC4
Associated Variants
XRCC4 p.Ala56Thr (p.A56T) ( ENST00000282268.7, ENST00000338635.10, ENST00000396027.9, ENST00000511817.1 )
XRCC4 p.Ala56Thr (p.A56T) ( ENST00000282268.7, ENST00000338635.10, ENST00000396027.9, ENST00000511817.1 )
Associated Disease
Short stature, microcephaly, and endocrine dysfunction
Source Database
ClinVar
Description
NM_003401.5(XRCC4):c.166G>A (p.Ala56Thr) AND Short stature, microcephaly, and endocrine dysfunction
ClinVar Allele ID
1297623
ClinVar RefSeq Alternation Syntax
NM_001318013.2:c.166G>A
ClinVar RefSeq Alternation Syntax
NM_022406.5:c.166G>A
ClinVar RefSeq Alternation Syntax
NM_001318012.3:c.166G>A
ClinVar RefSeq Alternation Syntax
NM_022550.4:c.166G>A
ClinVar RefSeq Alternation Syntax
NM_003401.5:c.166G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2022-03-29
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002488558
ClinVar Disease
Short stature, microcephaly, and endocrine dysfunction
Observed Origin Sample
unknown
Drugs