Annotation Detail

Information
Associated Genes
SH2B3
Associated Variants
SH2B3 p.Trp262Arg (p.W262R) ( ENST00000341259.7, ENST00000538307.1 )
SH2B3 p.Trp262Arg (p.W262R) ( ENST00000341259.7, ENST00000538307.1 )
Associated Disease
Primary myelofibrosis Thrombocythemia 1 Primary familial polycythemia due to EPO receptor mutation
Source Database
ClinVar
Description
NM_005475.3(SH2B3):c.784T>C (p.Trp262Arg) AND multiple conditions
ClinVar Allele ID
1254915
ClinVar RefSeq Alternation Syntax
NM_001291424.1:c.178T>C
ClinVar RefSeq Alternation Syntax
NM_005475.3:c.784T>C
Clinical Significance Description
Benign
Clinical Significance Last Update
2022-05-16
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002488461
ClinVar Disease
Primary myelofibrosis
ClinVar Disease
Thrombocythemia 1
ClinVar Disease
Primary familial polycythemia due to EPO receptor mutation
Observed Origin Sample
unknown
Drugs