Annotation Detail

Information
Associated Genes
HRAS LRRC56
Associated Variants
HRAS p.Gly13Asp (p.G13D) ( ENST00000311189.8, ENST00000397594.7, ENST00000397596.6, ENST00000417302.7, ENST00000451590.5 )
HRAS p.Gly13Asp (p.G13D) ( ENST00000311189.8, ENST00000397594.7, ENST00000397596.6, ENST00000417302.7, ENST00000451590.5 )
Associated Disease
Costello syndrome linear nevus sebaceous syndrome Malignant tumor of urinary bladder large congenital melanocytic nevus epidermal nevus Thyroid cancer, nonmedullary, 2
Source Database
ClinVar
Description
NM_005343.4(HRAS):c.38G>A (p.Gly13Asp) AND multiple conditions
ClinVar Allele ID
27643
ClinVar RefSeq Alternation Syntax
NM_176795.5:c.38G>A
ClinVar RefSeq Alternation Syntax
NM_001130442.3:c.38G>A
ClinVar RefSeq Alternation Syntax
NM_005343.4:c.38G>A
ClinVar RefSeq Alternation Syntax
NM_001318054.2:c.-282G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-03-10
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002476960
ClinVar Disease
Linear nevus sebaceous syndrome
ClinVar Disease
Malignant tumor of urinary bladder
ClinVar Disease
Thyroid cancer, nonmedullary, 2
ClinVar Disease
Large congenital melanocytic nevus
ClinVar Disease
Costello syndrome
ClinVar Disease
Epidermal nevus
Observed Origin Sample
unknown
Drugs