Annotation Detail

Information
Associated Genes
VHL
Associated Variants
VHL p.Pro81Ser (p.P81S) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
VHL p.Pro81Ser (p.P81S) ( ENST00000256474.3, ENST00000345392.3, ENST00000696143.2, ENST00000696153.1, ENST00000713811.1, ENST00000713812.1, ENST00000713815.1, ENST00000713982.1 )
Associated Disease
Enchondromatosis
Source Database
ClinVar
Description
NM_000551.4(VHL):c.241C>T (p.Pro81Ser) AND Enchondromatosis
ClinVar Allele ID
17272
ClinVar RefSeq Alternation Syntax
NM_001354723.2:c.241C>T
ClinVar RefSeq Alternation Syntax
NM_198156.3:c.241C>T
ClinVar RefSeq Alternation Syntax
NM_000551.4:c.241C>T
Clinical Significance Description
no classifications from unflagged records
Clinical Significance Last Update
2023-10-12
Clinical Significance Review Status
no classifications from unflagged records
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002467489
ClinVar Disease
Enchondromatosis
Observed Origin Sample
paternal
Drugs