Annotation Detail

Information
Associated Genes
RB1
Associated Variants
RB1 p.Cys712Arg (p.C712R) ( ENST00000713858.1, ENST00000713857.1, ENST00000650461.1, ENST00000267163.6, ENST00000713856.1 )
RB1 p.Cys712Arg (p.C712R) ( ENST00000267163.6, ENST00000650461.1, ENST00000713856.1, ENST00000713857.1, ENST00000713858.1 )
Associated Disease
Hereditary retinoblastoma
Source Database
ClinVar
Description
NM_000321.3(RB1):c.2134T>C (p.Cys712Arg) AND Hereditary retinoblastoma
ClinVar Allele ID
28131
ClinVar RefSeq Alternation Syntax
NM_000321.3:c.2134T>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2019-11-21
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002466401
ClinVar Disease
Hereditary retinoblastoma
Observed Origin Sample
germline
Drugs