Annotation Detail

Information
Associated Genes
HNF1B LOC126862549
Associated Variants
HNF1B p.Tyr250= (p.Y250=) ( ENST00000614313.4, ENST00000621123.4, ENST00000613727.4, ENST00000617811.5 )
HNF1B p.Tyr250= (p.Y250=) ( ENST00000613727.4, ENST00000614313.4, ENST00000617811.5, ENST00000621123.4 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
ClinVar
Description
NM_000458.4(HNF1B):c.750C>T (p.Tyr250=) AND Maturity onset diabetes mellitus in young
ClinVar Allele ID
45514
ClinVar RefSeq Alternation Syntax
NM_001165923.4:c.672C>T
ClinVar RefSeq Alternation Syntax
NM_001304286.2:c.672C>T
ClinVar RefSeq Alternation Syntax
NM_000458.4:c.750C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002464088
ClinVar Disease
Maturity onset diabetes mellitus in young
Observed Origin Sample
unknown
Drugs