Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Tyr122Cys (p.Y122C) ( ENST00000541395.5, ENST00000544413.2, ENST00000257555.11, ENST00000400024.6 )
HNF1A p.Tyr122Cys (p.Y122C) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.365A>G (p.Tyr122Cys) AND Maturity onset diabetes mellitus in young
ClinVar Allele ID
29969
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.365A>G
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.365A>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002464065
ClinVar Disease
Maturity onset diabetes mellitus in young
Observed Origin Sample
unknown
Drugs