Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Ile27Leu (p.I27L) ( ENST00000541395.5, ENST00000257555.11, ENST00000400024.6, ENST00000544413.2 )
HNF1A p.Ile27Leu (p.I27L) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.79A>C (p.Ile27Leu) AND Maturity onset diabetes mellitus in young
ClinVar Allele ID
29976
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.79A>C
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.79A>C
Clinical Significance Description
Benign
Clinical Significance Last Update
2015-08-19
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002415417
ClinVar Disease
Maturity onset diabetes mellitus in young
Observed Origin Sample
germline
Drugs