Annotation Detail

Information
Associated Genes
RB1
Associated Variants
RB1 p.Tyr606Ter (p.Y606*) ( ENST00000713858.1, ENST00000713857.1, ENST00000650461.1, ENST00000267163.6, ENST00000713856.1 )
RB1 p.Tyr606Ter (p.Y606*) ( ENST00000267163.6, ENST00000650461.1, ENST00000713856.1, ENST00000713857.1, ENST00000713858.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000321.3(RB1):c.1818T>A (p.Tyr606Ter) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
28133
ClinVar RefSeq Alternation Syntax
NM_000321.3:c.1818T>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2017-08-04
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002408459
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs