Annotation Detail

Information
Associated Genes
KCNQ1
Associated Variants
KCNQ1 p.Thr322Arg (p.T322R) ( ENST00000335475.6, ENST00000646564.2, ENST00000713725.1, ENST00000496887.7, ENST00000155840.12 )
KCNQ1 p.Thr322Arg (p.T322R) ( ENST00000155840.12, ENST00000335475.6, ENST00000496887.7, ENST00000646564.2, ENST00000713725.1 )
Source Database
ClinVar
Description
NM_000218.3(KCNQ1):c.965C>G (p.Thr322Arg) AND Cardiovascular phenotype
ClinVar Allele ID
197455
ClinVar RefSeq Alternation Syntax
NM_001406837.1:c.695C>G
ClinVar RefSeq Alternation Syntax
NM_000218.3:c.965C>G
ClinVar RefSeq Alternation Syntax
NM_001406838.1:c.521C>G
ClinVar RefSeq Alternation Syntax
NM_181798.2:c.584C>G
ClinVar RefSeq Alternation Syntax
NM_001406836.1:c.965C>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2021-09-14
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002372112
Observed Origin Sample
germline
Drugs