Annotation Detail

Information
Associated Genes
POLG FANCI POLGARF
Associated Variants
POLG p.Gln1236His (p.Q1236H), FANCI c.*304C>A ( ENST00000696718.1, ENST00000442287.6, ENST00000268124.11, ENST00000636937.2, ENST00000696719.1, ENST00000696717.1, ENST00000676003.1, ENST00000300027.12, ENST00000310775.12 )
POLG p.Gln1236His (p.Q1236H), FANCI c.*304C>A ( ENST00000268124.11, ENST00000442287.6, ENST00000636937.2, ENST00000300027.12, ENST00000310775.12, ENST00000676003.1, ENST00000696717.1, ENST00000696718.1, ENST00000696719.1 )
Associated Disease
Inborn genetic diseases
Source Database
ClinVar
Description
NM_002693.3(POLG):c.3708G>T (p.Gln1236His) AND Inborn genetic diseases
ClinVar Allele ID
34168
ClinVar RefSeq Alternation Syntax
NM_002693.3:c.3708G>T
ClinVar RefSeq Alternation Syntax
NM_001376911.1:c.*304C>A
ClinVar RefSeq Alternation Syntax
NM_001113378.2:c.*304C>A
ClinVar RefSeq Alternation Syntax
NM_018193.3:c.*304C>A
ClinVar RefSeq Alternation Syntax
NM_001376910.1:c.*304C>A
ClinVar RefSeq Alternation Syntax
NM_001126131.2:c.3708G>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2016-03-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002311519
ClinVar Disease
Inborn genetic diseases
Observed Origin Sample
germline
Drugs