Annotation Detail

Information
Associated Genes
HBB LOC106099062 LOC107133510
Associated Variants
HBB p.Glu27Lys (p.E27K) ( ENST00000485743.1, ENST00000335295.4, ENST00000647020.1 )
HBB p.Glu27Lys (p.E27K) ( ENST00000335295.4, ENST00000485743.1, ENST00000647020.1 )
Associated Disease
Beta-thalassemia HBB/LCRB
Source Database
ClinVar
Description
NM_000518.5(HBB):c.79G>A (p.Glu27Lys) AND Beta-thalassemia HBB/LCRB
ClinVar Allele ID
30200
ClinVar RefSeq Alternation Syntax
NM_000518.5:c.79G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2024-01-05
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002288495
ClinVar Disease
Beta-thalassemia HBB/LCRB
Observed Origin Sample
germline
Observed Origin Sample
unknown
Drugs