Annotation Detail

Information
Associated Genes
PKHD1 LOC126859690
Associated Variants
PKHD1 p.Val1741Met (p.V1741M) ( ENST00000340994.4, ENST00000371117.8 )
PKHD1 p.Val1741Met (p.V1741M) ( ENST00000340994.4, ENST00000371117.8 )
Associated Disease
Kidney disorder
Source Database
ClinVar
Description
NM_138694.4(PKHD1):c.5221G>A (p.Val1741Met) AND Kidney disorder
ClinVar Allele ID
19150
ClinVar RefSeq Alternation Syntax
NM_138694.4:c.5221G>A
ClinVar RefSeq Alternation Syntax
NM_170724.3:c.5221G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2021-12-21
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002287323
ClinVar Disease
Kidney disorder
Observed Origin Sample
unknown
Drugs