Annotation Detail

Information
Associated Genes
NBN
Associated Variants
NBN p.Lys219AsnfsTer16 (p.K219Nfs*16) ( ENST00000265433.8, ENST00000409330.5, ENST00000517337.2, ENST00000523444.2, ENST00000697292.1, ENST00000697293.1, ENST00000697298.1, ENST00000697299.1, ENST00000697304.1, ENST00000697307.1, ENST00000697308.1, ENST00000697309.1, ENST00000697310.1 )
NBN p.Lys219AsnfsTer16 (p.K219Nfs*16) ( ENST00000265433.8, ENST00000409330.5, ENST00000517337.2, ENST00000523444.2, ENST00000697292.1, ENST00000697293.1, ENST00000697298.1, ENST00000697299.1, ENST00000697304.1, ENST00000697307.1, ENST00000697308.1, ENST00000697309.1, ENST00000697310.1 )
Associated Disease
hepatocellular carcinoma
Source Database
ClinVar
Description
NM_002485.5(NBN):c.657_661del (p.Lys219fs) AND Hepatocellular carcinoma
ClinVar Allele ID
21979
ClinVar RefSeq Alternation Syntax
NM_002485.5:c.657_661del
ClinVar RefSeq Alternation Syntax
NM_001024688.3:c.411_415del
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2022-05-17
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002280859
ClinVar Disease
Hepatocellular carcinoma
Observed Origin Sample
germline
Drugs