Annotation Detail

Information
Associated Genes
TTC7A
Associated Variants
TTC7A p.Glu96Ter (p.E96*) ( ENST00000319190.11, ENST00000394850.6, ENST00000409245.5 )
TTC7A p.Glu96Ter (p.E96*) ( ENST00000319190.11, ENST00000394850.6, ENST00000409245.5 )
Associated Disease
Gastrointestinal defects and immunodeficiency syndrome 1
Source Database
ClinVar
Description
NM_020458.4(TTC7A):c.286G>T (p.Glu96Ter) AND Gastrointestinal defects and immunodeficiency syndrome 1
ClinVar Allele ID
268384
ClinVar RefSeq Alternation Syntax
NM_001288953.2:c.184G>T
ClinVar RefSeq Alternation Syntax
NM_001288951.2:c.286G>T
ClinVar RefSeq Alternation Syntax
NM_001288955.2:c.-619G>T
ClinVar RefSeq Alternation Syntax
NM_020458.4:c.286G>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-02-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002272204
ClinVar Disease
Gastrointestinal defects and immunodeficiency syndrome 1
Observed Origin Sample
germline
Drugs