Annotation Detail

Information
Associated Genes
COL5A1 LOC101448202
Associated Variants
COL5A1 c.*267C>T ( ENST00000371817.8, ENST00000371820.4 )
COL5A1 c.*267C>T ( ENST00000371817.8, ENST00000371820.4 )
Associated Disease
Ehlers-Danlos syndrome, classic type, 1
Source Database
ClinVar
Description
NM_000093.5(COL5A1):c.*267C>T AND Ehlers-Danlos syndrome, classic type, 1
ClinVar Allele ID
317325
ClinVar RefSeq Alternation Syntax
NM_001278074.1:c.*267C>T
ClinVar RefSeq Alternation Syntax
NM_000093.5:c.*267C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2022-03-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002270231
ClinVar Disease
Ehlers-Danlos syndrome, classic type, 1
Observed Origin Sample
germline
Drugs