Annotation Detail

Information
Associated Genes
TNFRSF1A
Associated Variants
TNFRSF1A p.Pro75Leu (p.P75L) ( ENST00000440083.7, ENST00000162749.7, ENST00000540022.5 )
TNFRSF1A p.Pro75Leu (p.P75L) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
Associated Disease
Autoinflammatory syndrome
Source Database
ClinVar
Description
NM_001065.4(TNFRSF1A):c.224C>T (p.Pro75Leu) AND Autoinflammatory syndrome
ClinVar Allele ID
244836
ClinVar RefSeq Alternation Syntax
NM_001065.4:c.224C>T
ClinVar RefSeq Alternation Syntax
NR_144351.2:n.486C>T
ClinVar RefSeq Alternation Syntax
NM_001346091.2:c.-101C>T
ClinVar RefSeq Alternation Syntax
NM_001346092.2:c.-354C>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2022-04-19
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002262855
ClinVar Disease
Autoinflammatory syndrome
Observed Origin Sample
germline
Drugs