Annotation Detail

Information
Associated Genes
TNFRSF1A
Associated Variants
TNFRSF1A p.Arg121Gln (p.R121Q) ( ENST00000440083.7, ENST00000540022.5, ENST00000162749.7 )
TNFRSF1A p.Arg121Gln (p.R121Q) ( ENST00000162749.7, ENST00000440083.7, ENST00000540022.5 )
Associated Disease
Autoinflammatory syndrome
Source Database
ClinVar
Description
NM_001065.4(TNFRSF1A):c.362G>A (p.Arg121Gln) AND Autoinflammatory syndrome
ClinVar Allele ID
213624
ClinVar RefSeq Alternation Syntax
NR_144351.2:n.624G>A
ClinVar RefSeq Alternation Syntax
NM_001346091.2:c.38G>A
ClinVar RefSeq Alternation Syntax
NM_001346092.2:c.-216G>A
ClinVar RefSeq Alternation Syntax
NM_001065.4:c.362G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2020-04-05
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002262795
ClinVar Disease
Autoinflammatory syndrome
Observed Origin Sample
germline
Drugs