Annotation Detail

Information
Associated Genes
PTCH1 LOC100507346
Associated Variants
PTCH1 p.Ala578= (p.A578=) ( ENST00000331920.11, ENST00000429896.6, ENST00000430669.6, ENST00000437951.6, ENST00000692981.1, ENST00000711046.1 )
PTCH1 p.Ala578= (p.A578=) ( ENST00000331920.11, ENST00000429896.6, ENST00000430669.6, ENST00000437951.6, ENST00000692981.1, ENST00000711046.1 )
Associated Disease
Hereditary cancer-predisposing syndrome
Source Database
ClinVar
Description
NM_000264.5(PTCH1):c.1734G>A (p.Ala578=) AND Hereditary cancer-predisposing syndrome
ClinVar Allele ID
221910
ClinVar RefSeq Alternation Syntax
NM_001083604.3:c.1281G>A
ClinVar RefSeq Alternation Syntax
NM_001083602.3:c.1536G>A
ClinVar RefSeq Alternation Syntax
NM_001083603.3:c.1731G>A
ClinVar RefSeq Alternation Syntax
NM_001083605.3:c.1281G>A
ClinVar RefSeq Alternation Syntax
NM_001083606.3:c.1281G>A
ClinVar RefSeq Alternation Syntax
NM_001354918.2:c.1578G>A
ClinVar RefSeq Alternation Syntax
NR_038982.1:n.1864C>T
ClinVar RefSeq Alternation Syntax
NR_149061.2:n.2639G>A
ClinVar RefSeq Alternation Syntax
NM_001083607.3:c.1281G>A
ClinVar RefSeq Alternation Syntax
NM_000264.5:c.1734G>A
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2020-10-23
Clinical Significance Review Status
criteria provided, multiple submitters, no conflicts
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002256117
ClinVar Disease
Hereditary cancer-predisposing syndrome
Observed Origin Sample
germline
Drugs