Annotation Detail

Information
Associated Genes
TERT
Associated Variants
TERT p.His412Tyr (p.H412Y) ( ENST00000310581.10, ENST00000334602.10 )
TERT p.His412Tyr (p.H412Y) ( ENST00000310581.10, ENST00000334602.10 )
Associated Disease
dyskeratosis congenita
Source Database
ClinVar
Description
NM_198253.3(TERT):c.1234C>T (p.His412Tyr) AND Dyskeratosis congenita
ClinVar Allele ID
27769
ClinVar RefSeq Alternation Syntax
NR_149162.3:n.1313C>T
ClinVar RefSeq Alternation Syntax
NM_001193376.3:c.1234C>T
ClinVar RefSeq Alternation Syntax
NR_149163.3:n.1313C>T
ClinVar RefSeq Alternation Syntax
NM_198253.3:c.1234C>T
Clinical Significance Description
Benign
Clinical Significance Last Update
2020-03-26
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002255259
ClinVar Disease
Dyskeratosis congenita
Observed Origin Sample
germline
Drugs