Annotation Detail

Information
Associated Genes
HNF1A
Associated Variants
HNF1A p.Ala276Asp (p.A276D) ( ENST00000541395.5, ENST00000544413.2, ENST00000257555.11, ENST00000400024.6 )
HNF1A p.Ala276Asp (p.A276D) ( ENST00000257555.11, ENST00000400024.6, ENST00000541395.5, ENST00000544413.2 )
Associated Disease
Hyperinsulinism due to HNF1A deficiency
Source Database
ClinVar
Description
NM_000545.8(HNF1A):c.827C>A (p.Ala276Asp) AND Hyperinsulinism due to HNF1A deficiency
ClinVar Allele ID
29984
ClinVar RefSeq Alternation Syntax
NM_001306179.2:c.827C>A
ClinVar RefSeq Alternation Syntax
NM_000545.8:c.827C>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2020-01-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002254266
ClinVar Disease
Hyperinsulinism due to HNF1A deficiency
Observed Origin Sample
germline
Drugs