Annotation Detail

Information
Associated Genes
HNF1B
Associated Variants
NM_000458.4(HNF1B):c.544+1391T>C AND Maturity onset diabetes mellitus in young
HNF1B c.544+1391T>C ( ENST00000613727.4, ENST00000614313.4, ENST00000617811.5, ENST00000621123.4 )
Associated Disease
Maturity onset diabetes mellitus in young
Source Database
ClinVar
Description
NM_000458.4(HNF1B):c.544+1391T>C AND Maturity onset diabetes mellitus in young
ClinVar Allele ID
1679914
ClinVar RefSeq Alternation Syntax
NM_001165923.4:c.544+1391T>C
ClinVar RefSeq Alternation Syntax
NM_000458.4:c.544+1391T>C
ClinVar RefSeq Alternation Syntax
NM_001304286.2:c.544+1391T>C
Clinical Significance Description
Benign
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002251304
ClinVar Disease
Maturity onset diabetes mellitus in young
Observed Origin Sample
somatic
Drugs