Annotation Detail

Information
Associated Genes
KCNJ11
Associated Variants
KCNJ11 p.Ile182Val (p.I182V) ( ENST00000528731.1, ENST00000339994.5, ENST00000682350.1, ENST00000682764.1 )
KCNJ11 p.Ile182Val (p.I182V) ( ENST00000339994.5, ENST00000528731.1, ENST00000682350.1, ENST00000682764.1 )
Associated Disease
Transitory neonatal diabetes mellitus
Source Database
ClinVar
Description
NM_000525.4(KCNJ11):c.544A>G (p.Ile182Val) AND Transitory neonatal diabetes mellitus
ClinVar Allele ID
34050
ClinVar RefSeq Alternation Syntax
NM_001377296.1:c.283A>G
ClinVar RefSeq Alternation Syntax
NM_000525.4:c.544A>G
ClinVar RefSeq Alternation Syntax
NM_001166290.2:c.283A>G
ClinVar RefSeq Alternation Syntax
NM_001377297.1:c.283A>G
Clinical Significance Description
Benign
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002227045
ClinVar Disease
Transitory neonatal diabetes mellitus
Observed Origin Sample
somatic
Drugs