Annotation Detail

Information
Associated Genes
GP1BA
Associated Variants
GP1BA p.Asn57Asp (p.N57D) ( ENST00000649830.1, ENST00000329125.6 )
GP1BA p.Asn57Asp (p.N57D) ( ENST00000649830.1, ENST00000329125.6 )
Associated Disease
Bernard-Soulier syndrome, type A2, autosomal dominant
Source Database
ClinVar
Description
NM_000173.7(GP1BA):c.169A>G (p.Asn57Asp) AND Bernard-Soulier syndrome, type A2, autosomal dominant
ClinVar Allele ID
1668341
ClinVar RefSeq Alternation Syntax
NM_000173.7:c.169A>G
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV002222138
ClinVar Disease
Bernard-Soulier syndrome, type A2, autosomal dominant
Observed Origin Sample
unknown
Drugs