Annotation Detail

Information
Associated Genes
TCN2
Associated Variants
TCN2 p.Arg259His (p.R259H) ( ENST00000215838.8, ENST00000405742.7, ENST00000407817.3, ENST00000450638.5, ENST00000698263.1, ENST00000698265.1, ENST00000698266.1, ENST00000698268.1, ENST00000698270.1, ENST00000698271.1, ENST00000698272.1, ENST00000698273.1 )
TCN2 p.Arg259His (p.R259H) ( ENST00000215838.8, ENST00000405742.7, ENST00000407817.3, ENST00000450638.5, ENST00000698263.1, ENST00000698265.1, ENST00000698266.1, ENST00000698268.1, ENST00000698270.1, ENST00000698271.1, ENST00000698272.1, ENST00000698273.1 )
Associated Disease
transcobalamin II deficiency
Source Database
ClinVar
Description
NM_000355.4(TCN2):c.776G>A (p.Arg259His) AND Transcobalamin II deficiency
ClinVar Allele ID
1402898
ClinVar RefSeq Alternation Syntax
NM_001184726.2:c.695G>A
ClinVar RefSeq Alternation Syntax
NM_000355.4:c.776G>A
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2021-11-02
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001898181
ClinVar Disease
Transcobalamin II deficiency
Observed Origin Sample
germline
Drugs