Annotation Detail

Information
Associated Genes
EVC
Associated Variants
EVC p.Arg576Leu (p.R576L) ( ENST00000264956.11 )
EVC p.Arg576Leu (p.R576L) ( ENST00000264956.11 )
Associated Disease
Curry-Hall syndrome Ellis-Van Creveld syndrome
Source Database
ClinVar
Description
NM_153717.3(EVC):c.1727G>T (p.Arg576Leu) AND multiple conditions
ClinVar Allele ID
1341824
ClinVar RefSeq Alternation Syntax
NM_153717.3:c.1727G>T
ClinVar RefSeq Alternation Syntax
NM_001306090.2:c.1727G>T
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2021-12-12
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001897234
ClinVar Disease
Curry-Hall syndrome
ClinVar Disease
Ellis-van Creveld syndrome
Observed Origin Sample
germline
Drugs