Annotation Detail

Information
Associated Genes
PTEN
Associated Variants
PTEN p.Tyr46Cys (p.Y46C) ( ENST00000688308.1, ENST00000371953.8, ENST00000713839.1, ENST00000700021.1, ENST00000700029.2, ENST00000472832.3 )
PTEN p.Tyr46Cys (p.Y46C) ( ENST00000371953.8, ENST00000472832.3, ENST00000688308.1, ENST00000700021.1, ENST00000700029.2, ENST00000713839.1 )
Associated Disease
PTEN hamartoma tumor syndrome
Source Database
ClinVar
Description
NM_000314.8(PTEN):c.137A>G (p.Tyr46Cys) AND PTEN hamartoma tumor syndrome
ClinVar Allele ID
187333
ClinVar RefSeq Alternation Syntax
NM_001304718.2:c.-569A>G
ClinVar RefSeq Alternation Syntax
NM_001304717.5:c.656A>G
ClinVar RefSeq Alternation Syntax
NM_000314.8:c.137A>G
Clinical Significance Description
Uncertain significance
Clinical Significance Last Update
2021-01-31
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001874356
ClinVar Disease
PTEN hamartoma tumor syndrome
Observed Origin Sample
germline
Drugs