Annotation Detail

Information
Associated Genes
GLE1
Associated Variants
GLE1 p.Ile243Val (p.I243V) ( ENST00000309971.9, ENST00000372770.4, ENST00000683748.1, ENST00000684139.1, ENST00000684314.1, ENST00000684331.1, ENST00000684646.1 )
GLE1 p.Ile243Val (p.I243V) ( ENST00000309971.9, ENST00000372770.4, ENST00000683748.1, ENST00000684139.1, ENST00000684314.1, ENST00000684331.1, ENST00000684646.1 )
Associated Disease
Lethal congenital contractural syndrome Finnish type
Source Database
ClinVar
Description
NM_001003722.2(GLE1):c.727A>G (p.Ile243Val) AND Lethal congenital contractural syndrome Finnish type
ClinVar Allele ID
195270
ClinVar RefSeq Alternation Syntax
NM_001003722.2:c.727A>G
ClinVar RefSeq Alternation Syntax
NM_001499.2:c.727A>G
Clinical Significance Description
Benign
Clinical Significance Last Update
2019-11-20
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001833089
ClinVar Disease
Lethal congenital contractural syndrome Finnish type
Observed Origin Sample
germline
Drugs