Annotation Detail

Information
Associated Genes
ABCC8
Associated Variants
ABCC8 p.Tyr539Cys (p.Y539C) ( ENST00000683136.1, ENST00000647015.1, ENST00000642271.1, ENST00000302539.9, ENST00000644772.1, ENST00000646902.1, ENST00000643260.1, ENST00000684571.1, ENST00000389817.8 )
ABCC8 p.Tyr539Cys (p.Y539C) ( ENST00000302539.9, ENST00000389817.8, ENST00000642271.1, ENST00000643260.1, ENST00000644772.1, ENST00000646902.1, ENST00000647015.1, ENST00000683136.1, ENST00000684571.1 )
Associated Disease
Diabetes mellitus, transient neonatal, 2
Source Database
ClinVar
Description
NM_000352.6(ABCC8):c.1616A>G (p.Tyr539Cys) AND Diabetes mellitus, transient neonatal, 2
ClinVar Allele ID
44271
ClinVar RefSeq Alternation Syntax
NM_001351296.2:c.1613A>G
ClinVar RefSeq Alternation Syntax
NM_000352.6:c.1616A>G
ClinVar RefSeq Alternation Syntax
NM_001287174.3:c.1616A>G
ClinVar RefSeq Alternation Syntax
NR_147094.2:n.1682A>G
ClinVar RefSeq Alternation Syntax
NM_001351295.2:c.1616A>G
ClinVar RefSeq Alternation Syntax
NM_001351297.2:c.1613A>G
Clinical Significance Description
Uncertain significance
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001823102
ClinVar Disease
Diabetes mellitus, transient neonatal, 2
Observed Origin Sample
germline
Drugs