Annotation Detail

Information
Associated Genes
TGFBI
Associated Variants
TGFBI p.Arg124His (p.R124H) ( ENST00000442011.7 )
TGFBI p.Arg124His (p.R124H) ( ENST00000442011.7 )
Associated Disease
Lattice corneal dystrophy Type I
Source Database
ClinVar
Description
NM_000358.3(TGFBI):c.371G>A (p.Arg124His) AND Lattice corneal dystrophy Type I
ClinVar Allele ID
22908
ClinVar RefSeq Alternation Syntax
NM_000358.3:c.371G>A
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2022-01-03
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001807721
ClinVar Disease
Lattice corneal dystrophy Type I
Observed Origin Sample
germline
Drugs