Annotation Detail

Information
Associated Genes
CLPP
Associated Variants
CLPP p.Ile100Thr (p.I100T) ( ENST00000245816.11, ENST00000596149.5 )
CLPP p.Ile100Thr (p.I100T) ( ENST00000245816.11, ENST00000596149.5 )
Associated Disease
Perrault syndrome 3
Source Database
ClinVar
Description
NM_006012.4(CLPP):c.299T>C (p.Ile100Thr) AND Perrault syndrome 3
ClinVar Allele ID
1323530
ClinVar RefSeq Alternation Syntax
NM_006012.4:c.299T>C
Clinical Significance Description
Likely pathogenic
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001806386
ClinVar Disease
Perrault syndrome 3
Observed Origin Sample
inherited
Drugs