Annotation Detail

Information
Associated Genes
GNPTAB
Associated Variants
GNPTAB p.Arg587Ter (p.R587*) ( ENST00000299314.12 )
GNPTAB p.Arg587Ter (p.R587*) ( ENST00000299314.12 )
Associated Disease
mucolipidosis
Source Database
ClinVar
Description
NM_024312.5(GNPTAB):c.1759C>T (p.Arg587Ter) AND Mucolipidosis
ClinVar Allele ID
47643
ClinVar RefSeq Alternation Syntax
NM_024312.5:c.1759C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-10-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001778671
ClinVar Disease
Mucolipidosis
Observed Origin Sample
germline
Drugs