Annotation Detail

Information
Associated Genes
ITPA
Associated Variants
ITPA c.124+21A>C ( ENST00000380113.8, ENST00000399838.3, ENST00000455664.6 )
ITPA c.124+21A>C ( ENST00000380113.8, ENST00000399838.3, ENST00000455664.6 )
Associated Disease
Developmental and epileptic encephalopathy, 35
Source Database
ClinVar
Description
NM_033453.4(ITPA):c.124+21A>C AND Developmental and epileptic encephalopathy, 35
ClinVar Allele ID
29786
ClinVar RefSeq Alternation Syntax
NM_001324237.2:c.-214+21A>C
ClinVar RefSeq Alternation Syntax
NM_033453.4:c.124+21A>C
ClinVar RefSeq Alternation Syntax
NM_001324236.2:c.-274-11A>C
ClinVar RefSeq Alternation Syntax
NM_001351739.2:c.-274-11A>C
ClinVar RefSeq Alternation Syntax
NM_001267623.2:c.67-738A>C
ClinVar RefSeq Alternation Syntax
NM_001324238.2:c.-274-11A>C
ClinVar RefSeq Alternation Syntax
NM_181493.4:c.73+21A>C
ClinVar RefSeq Alternation Syntax
NM_001324240.2:c.124+21A>C
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-08-19
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001730474
ClinVar Disease
Developmental and epileptic encephalopathy, 35
Observed Origin Sample
germline
Drugs