Annotation Detail

Information
Associated Genes
COASY
Associated Variants
COASY p.Thr353= (p.T353=) ( ENST00000421097.6, ENST00000393818.3, ENST00000590958.5 )
COASY p.Thr353= (p.T353=) ( ENST00000393818.3, ENST00000421097.6, ENST00000590958.5 )
Associated Disease
Pontocerebellar hypoplasia, type 12
Source Database
ClinVar
Description
NM_025233.7(COASY):c.972A>G (p.Thr324=) AND Pontocerebellar hypoplasia, type 12
ClinVar Allele ID
378199
ClinVar RefSeq Alternation Syntax
NM_001042529.3:c.972A>G
ClinVar RefSeq Alternation Syntax
NM_025233.7:c.972A>G
ClinVar RefSeq Alternation Syntax
NM_001042532.4:c.1059A>G
Clinical Significance Description
Benign
Clinical Significance Last Update
2021-07-22
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001584117
ClinVar Disease
Pontocerebellar hypoplasia, type 12
Observed Origin Sample
germline
Drugs