Annotation Detail

Information
Associated Genes
LARS2
Associated Variants
LARS2 p.Thr629Met (p.T629M) ( ENST00000414984.5, ENST00000642274.1, ENST00000645846.2, ENST00000650792.2 )
LARS2 p.Thr629Met (p.T629M) ( ENST00000414984.5, ENST00000642274.1, ENST00000645846.2, ENST00000650792.2 )
Associated Disease
Nonsyndromic genetic hearing loss
Source Database
ClinVar
Description
NM_015340.4(LARS2):c.1886C>T (p.Thr629Met) AND Nonsyndromic genetic hearing loss
ClinVar Allele ID
70523
ClinVar RefSeq Alternation Syntax
NM_015340.4:c.1886C>T
ClinVar RefSeq Alternation Syntax
NM_001368263.1:c.1886C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2021-07-15
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001544530
ClinVar Disease
Nonsyndromic genetic hearing loss
Observed Origin Sample
germline
Drugs