Annotation Detail

Information
Associated Genes
ACTA2 FAS
Associated Variants
ACTA2 c.-24+733T>C ( ENST00000713602.1, ENST00000458159.6, ENST00000415557.2 )
ACTA2 c.-24+733T>C ( ENST00000415557.2, ENST00000458159.6, ENST00000713602.1, ENST00000690268.1 )
Associated Disease
Autoimmune lymphoproliferative syndrome type 1
Source Database
ClinVar
Description
NM_001141945.3(ACTA2):c.-24+733T>C AND Autoimmune lymphoproliferative syndrome type 1
ClinVar Allele ID
712501
ClinVar RefSeq Alternation Syntax
NM_001320855.2:c.-24+816T>C
ClinVar RefSeq Alternation Syntax
NM_001406467.1:c.-24+816T>C
ClinVar RefSeq Alternation Syntax
NM_001406463.1:c.-182+733T>C
ClinVar RefSeq Alternation Syntax
NM_001406468.1:c.-24+733T>C
ClinVar RefSeq Alternation Syntax
NM_001141945.3:c.-24+733T>C
ClinVar RefSeq Alternation Syntax
NM_001406471.1:c.-24+733T>C
ClinVar RefSeq Alternation Syntax
NM_001406462.1:c.-182+816T>C
Clinical Significance Description
Benign
Clinical Significance Last Update
2020-12-06
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001515574
ClinVar Disease
Autoimmune lymphoproliferative syndrome type 1
Observed Origin Sample
germline
Drugs