Annotation Detail

Information
Associated Genes
EVC
Associated Variants
EVC p.Arg576Gln (p.R576Q) ( ENST00000264956.11 )
EVC p.Arg576Gln (p.R576Q) ( ENST00000264956.11 )
Associated Disease
Ellis-Van Creveld syndrome Curry-Hall syndrome
Source Database
ClinVar
Description
NM_153717.3(EVC):c.1727G>A (p.Arg576Gln) AND multiple conditions
ClinVar Allele ID
251543
ClinVar RefSeq Alternation Syntax
NM_153717.3:c.1727G>A
ClinVar RefSeq Alternation Syntax
NM_001306090.2:c.1727G>A
Clinical Significance Description
Benign
Clinical Significance Last Update
2024-02-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001511705
ClinVar Disease
Curry-Hall syndrome
ClinVar Disease
Ellis-van Creveld syndrome
Observed Origin Sample
germline
Drugs