Annotation Detail

Information
Associated Genes
MRE11
Associated Variants
MRE11 p.Thr439= (p.T439=) ( ENST00000323929.8, ENST00000393241.8, ENST00000407439.7, ENST00000323977.7 )
MRE11 p.Thr439= (p.T439=) ( ENST00000323929.8, ENST00000323977.7, ENST00000393241.8, ENST00000407439.7 )
Associated Disease
Ataxia-telangiectasia-like disorder
Source Database
ClinVar
Description
NM_005591.4(MRE11):c.1317C>T (p.Thr439=) AND Ataxia-telangiectasia-like disorder
ClinVar Allele ID
476411
ClinVar RefSeq Alternation Syntax
NM_005590.4:c.1317C>T
ClinVar RefSeq Alternation Syntax
NM_005591.4:c.1317C>T
ClinVar RefSeq Alternation Syntax
NM_001330347.2:c.1317C>T
Clinical Significance Description
Likely benign
Clinical Significance Last Update
2022-09-26
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001478517
ClinVar Disease
Ataxia-telangiectasia-like disorder
Observed Origin Sample
germline
Drugs