Annotation Detail

Information
Associated Genes
COL7A1
Associated Variants
COL7A1 p.Arg236Ter (p.R236*) ( ENST00000328333.12, ENST00000681320.1 )
COL7A1 p.Arg236Ter (p.R236*) ( ENST00000328333.12, ENST00000681320.1 )
Associated Disease
epidermolysis bullosa dystrophica
Source Database
ClinVar
Description
NM_000094.4(COL7A1):c.706C>T (p.Arg236Ter) AND Epidermolysis bullosa dystrophica
ClinVar Allele ID
32501
ClinVar RefSeq Alternation Syntax
NM_000094.4:c.706C>T
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2014-04-01
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001352750
ClinVar Disease
Epidermolysis bullosa dystrophica
Observed Origin Sample
germline
Drugs