Annotation Detail

Information
Associated Genes
QARS1
Associated Variants
QARS1 p.Arg378Cys (p.R378C) ( ENST00000306125.12, ENST00000414533.5, ENST00000464962.6 )
QARS1 p.Arg378Cys (p.R378C) ( ENST00000306125.12, ENST00000414533.5, ENST00000464962.6 )
Associated Disease
Diffuse cerebral and cerebellar atrophy - intractable seizures - progressive microcephaly syndrome
Source Database
ClinVar
Description
NM_005051.3(QARS1):c.1132C>T (p.Arg378Cys) AND Diffuse cerebral and cerebellar atrophy - intractable seizures - progressive microcephaly syndrome
ClinVar Allele ID
590052
ClinVar RefSeq Alternation Syntax
NM_001272073.2:c.1099C>T
ClinVar RefSeq Alternation Syntax
NM_005051.3:c.1132C>T
ClinVar RefSeq Alternation Syntax
NR_073590.2:n.1107C>T
Clinical Significance Description
Conflicting interpretations of pathogenicity
Clinical Significance Last Update
2022-10-28
Clinical Significance Review Status
criteria provided, conflicting interpretations
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001299085
ClinVar Disease
Diffuse cerebral and cerebellar atrophy - intractable seizures - progressive microcephaly syndrome
Observed Origin Sample
germline
Observed Origin Sample
maternal
Drugs