Annotation Detail

Information
Associated Genes
F11
Associated Variants
F11 p.Gln134Ter (p.Q134*) ( ENST00000403665.7, ENST00000492972.6 )
F11 p.Gln134Ter (p.Q134*) ( ENST00000403665.7, ENST00000492972.6 )
Associated Disease
Plasma factor XI deficiency
Source Database
ClinVar
Description
NM_000128.4(F11):c.400C>T (p.Gln134Ter) AND Plasma factor XI deficiency
ClinVar Allele ID
186682
ClinVar RefSeq Alternation Syntax
NM_000128.4:c.400C>T
ClinVar RefSeq Alternation Syntax
NM_001354804.2:c.400C>T
Clinical Significance Description
Likely pathogenic
Clinical Significance Last Update
2020-09-16
Clinical Significance Review Status
no assertion criteria provided
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001273716
ClinVar Disease
Plasma factor XI deficiency
Observed Origin Sample
germline
Drugs