Annotation Detail

Information
Associated Genes
GJB2
Associated Variants
GJB2 p.Gly12ValfsTer2 (p.G12Vfs*2) ( ENST00000382848.5, ENST00000382844.2 )
GJB2 p.Gly12ValfsTer2 (p.G12Vfs*2) ( ENST00000382844.2, ENST00000382848.5 )
Associated Disease
Hearing loss, autosomal recessive
Source Database
ClinVar
Description
NM_004004.6(GJB2):c.35del (p.Gly12fs) AND Hearing loss, autosomal recessive
ClinVar Allele ID
32043
Clinical Significance Description
Pathogenic
Clinical Significance Last Update
2016-09-21
Clinical Significance Review Status
criteria provided, single submitter
URL
https://www.ncbi.nlm.nih.gov/clinvar/RCV001270107
ClinVar Disease
Hearing loss, autosomal recessive
Observed Origin Sample
germline
Observed Origin Sample
inherited
Drugs